Core entities
- Transposition of the Great Arteries (TGA)
- Double Outlet Right Ventricle (DORV)
- Tetralogy of Fallot (TOF)
- Congenitally Corrected Transposition of the Great Arteries
| Feature | Tetralogy of Fallot | Double Outlet Right Ventricle | Transposition of the Great Arteries |
|---|---|---|---|
| Great arteries | Crossing | Crossing or abnormal | Parallel |
| LV direct outlet | Yes (partly) | No | Yes (to PA) |
| Aortic override | 30–50% typical | >50% (often >70%) | None |
| VSD | Large malalignment | Always present | Variable |
| Pulmonary artery | Small | Variable | Normal |
| 3-vessel view | Small PA | Variable | Aorta anterior |
| LVOT continuity | Present | Absent | Present |
| RVOT obstruction | Typical | Variable | None |
| Feature | TGA | DORV | TOF | CCTGA |
|---|---|---|---|---|
| Great arteries | Parallel | Both from RV | Crossing | Parallel |
| LV connection | To PA | Often to VSD | To overriding aorta | To pulmonary artery |
| RV connection | To Aorta | To both vessels | To overriding aorta | To aorta |
| VSD | Required for survival | Always present | Always present | Variable |
| AV connections | Normal | Normal | Normal | Discordant |
A. Transposition of the Great Arteries (TGA)
Parallel great arteries
Outflow tract:
- Aorta arises from right ventricle
- Pulmonary artery arises from left ventricle
- No normal crossing
B. Double Outlet Right Ventricle (DORV)
Both great arteries arise predominantly from RV
VSD is mandatory.
LV has no direct outlet.
Instead: LV empties via VSD
Great arteries:
- crossing present
- abnormal alignment
C. Tetralogy of Fallot (TOF)
Classic tetrad:
- VSD
- Overriding aorta
- RV hypertrophy
- Pulmonary stenosis
Overriding aorta - Aorta sits: over VSD
Receiving blood from both ventricles.
Pulmonary artery: small
3-vessel view: Small pulmonary artery
D. Congenitally Corrected TGA (CCTGA)
Double discordance
- AV discordance
- VA discordance
Result: Circulation becomes "physiologically corrected."
Ventricular inversion
Right ventricle appears: on the left side
With:
- moderator band
- coarse trabeculation
Ventricular inversion
Great arteries:
Usually: parallel; Like TGA.
But: AV connections abnormal.